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This 11-year-old boy has very light skin, white hair, and light blue eyes. Both of his parents and two siblings, a brother and a sister, have skin that is fairly dark. The boy is bothered by bright sunlight and his skin burns easily in the sun. He has nystagmus and visual acuity reduced to 20/100 best corrected with glasses of OD -7.00, OS -8.00 as well as 35 prism diopters of exotropia.

1.	The condition that this boy has is likely to have been inherited as:
	a. autosomal dominant b. autosomal recessive c. X linked d. sporadic e. cannot be determined
2.	Tests to confirm the diagnosis or learn more about this condition include:
	a. skin biopsy b. iris trans-illumination c. fundus examination d. visual acuity testing e. all of the above
3.	Which of the following would be most likely to help this boy?
	a. no treatment; anything done would be likely to make him worse b. base in prism c. pin hole glasses d. an asymmetrical four muscle recession e. none of the above

For answers to the above, click here on or after June 10, 2008.