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A 22-year-old man presents with progressive decreased vision in both eyes for the past two years.  His visual acuity is 20/400 OU and he denies any prior eye surgery or disease.  His fundus and subsequent fluoroscein angiograms reveals the above clinical picture.

This disease is most likely caused by:

d -- genetic defect Stargardt's Disease Most commonly an autosomal recessive condition affecting young adults. The macula commonly appears atrophic with a "beaten metal appearance" and discreet yellow flecks. The pathogenesis appears to involve an accumulation of lipofuscin within the retinal pigment epithelium (RPE )