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1. Local causes
*A. Acne rosacea
B. Chronic congestive glaucoma
C. Delayed mustard gas keratitis
D. Idiopathic anomaly
E. Irradiation of the eye
F. Long-standing ocular inflammation
*G. Metastatic primary tumor
*H. Pterygium
*I. Underlying choroidal or ciliary body melanomas
2. Systemic causes
A. Acquired immunodeficiency syndrome (AIDS)
B. Arteriosclerosis
C. Associated with familial amyloidotic polyneuropathy, type 1
D. Ataxic telangiectasia (Louis-Bar syndrome)
*E. Degos syndrome (malignant atrophic papulosis)
F. Diabetes
G. Dysproteinemia as in Waldenström macroglobulinemia, cryoglobulinemia, and multiple myeloma
H. Endangiitis obliterans
I. Fabry disease (diffuse angiokeratosis)
J. Hereditary hemorrhagic telangiectasia (Rendu-Osler-Weber disease)
K. Hypertension
L. Klippel-Trenaunay-Weber syndrome (angioosteohypertrophy syndrome)
M. Normal individuals
*N. Pulmonary insufficiency
O. Reimann syndrome (hyperviscosity syndrome)
P. Renal failure
Q. Rheumatic fever or rheumatic heart disease
R. Scleroderma (progressive systemic sclerosis)
S. Sturge-Weber syndrome (meningocutaneous syndrome)
*T. Syphilis (acquired lues)
U. Varicose veins-generalized
Ando E, et al. Ocular microangiopathy in familial amyloidotic polyneuropathy, type 1. Graefes Arch Clin Exp Ophthalmol 1992; 230:1-5.
Baumann S, et al. Conjunctival microvasculopathy and Kaposi's sarcoma in patients with AIDS. AIDS 1994; 8: 134-135.
Roy FH. Ocular syndromes and systemic diseases, 3rd ed. Philadelphia: Lippincott Williams & Wilkins, 2002.
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